日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Fibin regulates cardiomyocyte hypertrophy and causes protein-aggregate-associated cardiomyopathy in vivo

Fibin 调节心肌细胞肥大,并在体内引起蛋白聚集相关性心肌病。

Petersen, Matthias; Schmiedel, Nesrin; Dierck, Franziska; Hille, Susanne; Remes, Anca; Senger, Frauke; Schmidt, Inga; Lüllmann-Rauch, Renate; Müller, Oliver J; Frank, Derk; Rangrez, Ashraf Y; Frey, Norbert; Kuhn, Christian

ADAM10-Mediated Ectodomain Shedding Is an Essential Driver of Podocyte Damage

ADAM10 介导的细胞外结构域脱落是足细胞损伤的重要驱动因素

Marlies Sachs, Sebastian Wetzel, Julia Reichelt, Wiebke Sachs, Lisa Schebsdat, Stephanie Zielinski, Lisa Seipold, Lukas Heintz, Stephan A Müller, Oliver Kretz, Maja Lindenmeyer, Thorsten Wiech, Tobias B Huber, Renate Lüllmann-Rauch, Stefan F Lichtenthaler, Paul Saftig, Catherine Meyer-Schwesinger

FYCO1 Regulates Cardiomyocyte Autophagy and Prevents Heart Failure Due to Pressure Overload In Vivo

FYCO1调节心肌细胞自噬并预防体内压力超负荷引起的心力衰竭

Kuhn, Christian; Menke, Maja; Senger, Frauke; Mack, Claudia; Dierck, Franziska; Hille, Susanne; Schmidt, Inga; Brunke, Gabriele; Bünger, Pia; Schmiedel, Nesrin; Will, Rainer; Sossalla, Samuel; Frank, Derk; Eschenhagen, Thomas; Carrier, Lucie; Lüllmann-Rauch, Renate; Rangrez, Ashraf Yusuf; Frey, Norbert

Enzyme replacement therapy with recombinant pro-CTSD (cathepsin D) corrects defective proteolysis and autophagy in neuronal ceroid lipofuscinosis

重组 pro-CTSD(组织蛋白酶 D)的酶替代疗法可纠正神经元蜡样脂褐素沉积症中的蛋白水解和自噬缺陷

André R A Marques, Alessandro Di Spiezio, Niklas Thießen, Lina Schmidt, Joachim Grötzinger, Renate Lüllmann-Rauch, Markus Damme, Steffen E Storck, Claus U Pietrzik, Jens Fogh, Julia Bär, Marina Mikhaylova, Markus Glatzel, Mahmoud Bassal, Udo Bartsch, Paul Saftig

Dysbindin deficiency Alters Cardiac BLOC-1 Complex and Myozap Levels in Mice

Dysbindin 缺乏会改变小鼠心脏 BLOC-1 复合物和 Myozap 水平

Ankush Borlepawar, Nesrin Schmiedel, Matthias Eden, Lynn Christen, Alexandra Rosskopf, Derk Frank, Renate Lüllmann-Rauch, Norbert Frey, Ashraf Yusuf Rangrez

Arylsulfatase K inactivation causes mucopolysaccharidosis due to deficient glucuronate desulfation of heparan and chondroitin sulfate

芳基硫酸酯酶K失活会导致粘多糖贮积症,这是由于肝素和硫酸软骨素的葡萄糖醛酸脱硫作用不足所致。

Trabszo, Christof; Ramms, Bastian; Chopra, Pradeep; Lüllmann-Rauch, Renate; Stroobants, Stijn; Sproß, Jens; Jeschke, Anke; Schinke, Thorsten; Boons, Geert-Jan; Esko, Jeffrey D; Lübke, Torben; Dierks, Thomas

Lysosomal integral membrane protein-2 (LIMP-2/SCARB2) is involved in lysosomal cholesterol export

溶酶体整合膜蛋白-2 (LIMP-2/SCARB2) 参与溶酶体胆固醇输出

Saskia Heybrock, Kristiina Kanerva, Ying Meng, Chris Ing, Anna Liang, Zi-Jian Xiong, Xialian Weng, Young Ah Kim, Richard Collins, William Trimble, Régis Pomès, Gilbert G Privé, Wim Annaert, Michael Schwake, Joerg Heeren, Renate Lüllmann-Rauch, Sergio Grinstein, Elina Ikonen, Paul Saftig, Dante Necul

The intramembrane protease SPPL2c promotes male germ cell development by cleaving phospholamban

膜内蛋白酶 SPPL2c 通过裂解受磷蛋白促进雄性生殖细胞发育

Johannes Niemeyer, Torben Mentrup, Ronny Heidasch, Stephan A Müller, Uddipta Biswas, Rieke Meyer, Alkmini A Papadopoulou, Verena Dederer, Martina Haug-Kröper, Vivian Adamski, Renate Lüllmann-Rauch, Martin Bergmann, Artur Mayerhofer, Paul Saftig, Gunther Wennemuth, Rolf Jessberger, Regina Fluhrer, St

The lysosomal transporter MFSD1 is essential for liver homeostasis and critically depends on its accessory subunit GLMP

溶酶体转运蛋白 MFSD1 对肝脏稳态至关重要,并且主要依赖于其附属亚基 GLMP

David Massa López, Melanie Thelen, Felix Stahl, Christian Thiel, Arne Linhorst, Marc Sylvester, Irm Hermanns-Borgmeyer, Renate Lüllmann-Rauch, Winnie Eskild, Paul Saftig, Markus Damme

Disruption of the vacuolar-type H+-ATPase complex in liver causes MTORC1-independent accumulation of autophagic vacuoles and lysosomes

肝脏中液泡型 H+-ATPase 复合物的破坏导致 MTORC1 独立的自噬液泡和溶酶体的积累

Sandra Kissing, Sönke Rudnik, Markus Damme, Renate Lüllmann-Rauch, Atsuhiro Ichihara, Uwe Kornak, Eeva-Liisa Eskelinen, Sabrina Jabs, Jörg Heeren, Jef K De Brabander, Albert Haas, Paul Saftig