日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A standardized framework resolves ambiguity in motor neuron loss across neurodegenerative diseases

标准化的框架可以消除神经退行性疾病中运动神经元丢失的模糊性

Sowoidnich, Leonie; Norman, Aaron L; Gerstner, Florian; Siemund, Josiane K; Buettner, Jannik M; Pagiazitis, John G; Dreilich, Vanessa; Pilz, Konstantin; Tian, Dajun; Sumner, Charlotte J; Paradis, Angela; Mentis, George Z; Simon, Christian M

Cerebellar pathology contributes to neurodevelopmental deficits in spinal muscular atrophy

小脑病变是脊髓性肌萎缩症神经发育缺陷的原因之一。

Gerstner, Florian; Wittig, Sandra; Menedo, Christian; Ruwald, Sayan; Carlini, Maria J; Vankova, Adela; Sowoidnich, Leonie; Martín-López, Gerardo; Dreilich, Vanessa; Alonso-Collado, Andrea; Pagiazitis, John G; Aousji, Oumayma; Grzyb, Chloe; Smith, Amy K; Yang, Mu; Roselli, Francesco; Mentis, George Z; Sumner, Charlotte J; Pellizzoni, Livio; Simon, Christian M

Synaptic imbalance and increased inhibition impair motor function in SMA.

SMA患者的突触失衡和抑制增强会损害运动功能

Fletcher Emily V, Chalif Joshua I, Rotterman Travis M, Pagiazitis John G, Van Alstyne Meaghan, Sivakumar Nandhini, Florez-Paz Danny, Rabinowitz Joseph E, Pellizzoni Livio, Alvarez Francisco J, Mentis George Z

Proprioceptive synaptic dysfunction is a key feature in mice and humans with spinal muscular atrophy

本体感觉突触功能障碍是小鼠和人类脊髓性肌萎缩症的一个关键特征。

Simon, Christian M; Delestrée, Nicolas; Montes, Jacqueline; Sowoidnich, Leonie; Gerstner, Florian; Carranza, Erick; Buettner, Jannik M; Pagiazitis, John G; Prat-Ortega, Genis; Ensel, Scott; Donadio, Serena; Dreilich, Vanessa; Carlini, Maria J; Garcia, Jose L; Kratimenos, Panagiotis; Chung, Wendy K; Sumner, Charlotte J; Weimer, Louis H; Pirondini, Elvira; Capogrosso, Marco; Pellizzoni, Livio; De Vivo, Darryl C; Mentis, George Z

SpIC3D imaging for spinal in situ contrast 3D visualization

SpIC3D成像用于脊柱原位对比剂三维可视化

Liang, Lucy; Fasse, Alessandro; Damiani, Arianna; Jantz, Maria K; Agbor, Uzoma; Del Brocco, Matteo; Monney, Rachel; Rowland, Cecelia; Newton, Taylor; Gopinath, Chaitanya; Schaeffer, David J; Kolarcik, Christi L; Pagiazitis, John G; Mentis, George Z; Fisher, Lee E; Neufeld, Esra; Capogrosso, Marco; Gaunt, Robert A; Hitchens, T Kevin; Pirondini, Elvira

Cerebellar pathology contributes to neurodevelopmental deficits in spinal muscular atrophy.

小脑病变是脊髓性肌萎缩症神经发育缺陷的原因之一

Gerstner Florian, Wittig Sandra, Menedo Christian, Ruwald Sayan, Carlini Maria J, Vankova Adela, Sowoidnich Leonie, Martín-López Gerardo, Dreilich Vanessa, Collado Andrea Alonso, Pagiazitis John G, Aousji Oumayma, Grzyb Chloe, Smith Amy, Yang Mu, Roselli Francesco, Mentis George Z, Sumner Charlotte J, Pellizzoni Livio, Simon Christian M

Serotonergic dysfunction impairs locomotor coordination in spinal muscular atrophy

血清素能功能障碍会损害脊髓性肌萎缩症患者的运动协调能力

Delestrée, Nicolas; Semizoglou, Evangelia; Pagiazitis, John G; Vukojicic, Aleksandra; Drobac, Estelle; Paushkin, Vasilissa; Mentis, George Z

Converging Mechanisms of p53 Activation Drive Motor Neuron Degeneration in Spinal Muscular Atrophy

p53激活的多种机制共同驱动脊髓性肌萎缩症中的运动神经元退化

Simon, Christian M; Dai, Ya; Van Alstyne, Meaghan; Koutsioumpa, Charalampia; Pagiazitis, John G; Chalif, Joshua I; Wang, Xiaojian; Rabinowitz, Joseph E; Henderson, Christopher E; Pellizzoni, Livio; Mentis, George Z

Sensory-Derived Glutamate Regulates Presynaptic Inhibitory Terminals in Mouse Spinal Cord

感觉神经元来源的谷氨酸调节小鼠脊髓突触前抑制性末梢

Mende, Michael; Fletcher, Emily V; Belluardo, Josephine L; Pierce, Joseph P; Bommareddy, Praveen K; Weinrich, Jarret A; Kabir, Zeeba D; Schierberl, Kathryn C; Pagiazitis, John G; Mendelsohn, Alana I; Francesconi, Anna; Edwards, Robert H; Milner, Teresa A; Rajadhyaksha, Anjali M; van Roessel, Peter J; Mentis, George Z; Kaltschmidt, Julia A