日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

ACAD10 and ACAD11 enable mammalian 4-hydroxy acid lipid catabolism.

ACAD10 和 ACAD11 能够促进哺乳动物 4-羟基酸脂质的分解代谢。

Rashan Edrees H, Bartlett Abigail K, Khana Daven B, Zhang Jingying, Jain Raghav, Wade Gina, Abriata Luciano A, Smith Andrew J, Baker Zakery N, Cook Taylor, Caldwell Alana, Chevalier Autumn R, Forny Patrick, Pfleger Brian F, Peraro Matteo Dal, Yuan Peng, Amador-Noguez Daniel, Simcox Judith A, Pagliarini David J

DFCP1 is a regulator of starvation-driven ATGL-mediated lipid droplet lipolysis

DFCP1 是饥饿驱动的 ATGL 介导的脂滴脂肪分解的调节剂

Victoria A Ismail, Meg Schuetz, Zak N Baker, Jean A Castillo-Badillo, Teri V Naismith, David J Pagliarini, David J Kast

Targeting TOMM40 and TOMM22 to Rescue Statin-Impaired Mitochondrial Function, Dynamics, and Mitophagy in Skeletal Myotubes

靶向TOMM40和TOMM22以挽救他汀类药物损害的骨骼肌细胞线粒体功能、动力学和线粒体自噬

Yang, Neil V; Rogers, Sean; Guerra, Rachel; Chao, Justin Y; Pagliarini, David J; Theusch, Elizabeth; Krauss, Ronald M

Mitochondrial dysfunction and lipid dysregulation in yeast lacking phosphatidylserine

缺乏磷脂酰丝氨酸的酵母中线粒体功能障碍和脂质代谢紊乱

Joshi, Alaumy; Baker, Zakery N; Stanfield, Rachel A; Kalafatis, Dimitris T; Pagliarini, David J; Gohil, Vishal M

Identification of a new COQ4 spliceogenic variant causing severe primary coenzyme Q deficiency

鉴定出一种新的COQ4剪接变异体,该变异体可导致严重的原发性辅酶Q缺乏症。

Alcázar-Fabra, María; Østergaard, Elsebet; Fernández-Ayala, Daniel J M; Desbats, María Andrea; Morbidoni, Valeria; Tomás-Gallado, Laura; García-Corzo, Laura; Blanquer-Roselló, María Del Mar; Bartlett, Abigail K; Sánchez-Cuesta, Ana; Sena, Lucía; Cortés-Rodríguez, Ana; Cascajo-Almenara, María Victoria; Pagliarini, David J; Trevisson, Eva; Gronborg, Sabine W; Brea-Calvo, Gloria

Severe Neurological Presentation in Siblings With COQ5-Related Primary Coenzyme Q10 Deficiency: Expanding Clinical and Molecular Spectrum

COQ5相关原发性辅酶Q10缺乏症患儿的严重神经系统表现:不断扩展的临床和分子谱

Wongkittichote, Parith; Guerra, Rachel M; Wegner, Daniel J; Toy, Samantha; Hauer, Jacqueline A; Pagliarini, David J; Granadillo, Jorge L

Uridine-sensitized screening identifies genes and metabolic regulators of nucleotide synthesis.

尿苷敏感筛选可识别核苷酸合成的基因和代谢调节因子

Strefeler Abigail, Baker Zakery N, Chollet Sylvain, Guerra Rachel M, Ivanisevic Julijana, Gallart-Ayala Hector, Pagliarini David J, Jourdain Alexis A

Mitochondrial proteome research: the road ahead

线粒体蛋白质组研究:未来之路

Baker, Zakery N; Forny, Patrick; Pagliarini, David J

Reducing mitochondrial mysteries

揭开线粒体之谜

Guerra, Rachel M; Pagliarini, David J

Coenzyme Q biochemistry and biosynthesis

辅酶Q的生物化学和生物合成

Guerra, Rachel M; Pagliarini, David J