日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Apolipoprotein E knockout, but not cholesteryl ester transfer protein (CETP)-associated high-density lipoprotein cholesterol (HDL-C) lowering, exacerbates muscle wasting in dysferlin-null mice

载脂蛋白 E 敲除(而非胆固醇酯转运蛋白 (CETP) 相关高密度脂蛋白胆固醇 (HDL-C) 降低)会加剧 dysferlin 基因缺失小鼠的肌肉萎缩

Zeren Sun, Zoe White, Marine Theret, Pascal Bernatchez

Cholesterol absorption blocker ezetimibe prevents muscle wasting in severe dysferlin-deficient and mdx mice

胆固醇吸收阻滞剂依折麦布可预防严重 dysferlin 缺乏和 mdx 小鼠的肌肉萎缩

Zoe White, Marine Theret, Nadia Milad, Lin Wei Tung, William Wei-Han Chen, Martin G Sirois, Fabio Rossi, Pascal Bernatchez

Limb-girdle muscular dystrophy type 2B causes HDL-C abnormalities in patients and statin-resistant muscle wasting in dysferlin-deficient mice

肢带型肌营养不良症2B型会导致患者高密度脂蛋白胆固醇(HDL-C)异常,并在缺乏dysferlin蛋白的小鼠中引起他汀类药物抵抗性肌肉萎缩。

Zoe White # ,Zeren Sun # ,Elodie Sauge ,Dan Cox ,Graham Donen ,Dmitri Pechkovsky ,Volker Straub ,Gordon A Francis ,Pascal Bernatchez

A Role of Caveolae in Trabecular Meshwork Mechanosensing and Contractile Tone

小窝在小梁网机械传感和收缩张力中的作用

Michael L De Ieso, Megan Kuhn, Pascal Bernatchez, Michael H Elliott, W Daniel Stamer

Pleiotropic activation of endothelial function by angiotensin II receptor blockers is crucial to their protective anti-vascular remodeling effects

血管紧张素 II 受体阻滞剂对内皮功能的多效激活对其保护性抗血管重塑作用至关重要

Arash Y Tehrani, Zoe White, Lin Wei Tung, Roy Ru Yi Zhao, Nadia Milad, Michael A Seidman, Elodie Sauge, Marine Theret, Fabio M V Rossi, Mitra Esfandiarei, Casey van Breemen, Pascal Bernatchez

Thermoneutral Housing and a Western Diet Combination Exacerbates Dysferlin-Deficient Muscular Dystrophy

热中性住房和西方饮食组合加剧 Dysferlin 缺乏性肌营养不良症

Graham S Donen, Zoe White, Elodie Sauge, Morten Ritso, Marine Theret, John Boyd, Angela M Devlin, Fabio M V Rossi, Pascal Bernatchez

Effect of Dysferlin Deficiency on Atherosclerosis and Plasma Lipoprotein Composition Under Normal and Hyperlipidemic Conditions

肌营养不良蛋白缺乏对正常和高脂血症条件下动脉粥样硬化和血浆脂蛋白组成的影响

Zoe White ,Nadia Milad ,Stephanie L Sellers ,Pascal Bernatchez

Characterization of doxycycline-mediated inhibition of Marfan syndrome-associated aortic dilation by multiphoton microscopy

通过多光子显微镜表征强力霉素介导的马凡氏综合征相关主动脉扩张的抑制

Arash Y Tehrani #, Jason Z Cui #, T Bucky Jones, Ester Hotova, Monica Castro, Pascal Bernatchez, Cornelis van Breemen, Mitra Esfandiarei

Aortic Dimensions, Biophysical Properties, and Plasma Biomarkers in Children and Adults with Marfan or Loeys-Dietz Syndrome

患有马凡氏综合征或 Loeys-Dietz 综合征的儿童和成人的主动脉尺寸、生物物理特性和血浆生物标志物

Jason Z Cui, Kevin C Harris, Koen Raedschelders, Zsuzsanna Hollander, James E Potts, Astrid De Souza, Marla Kiess, Bruce M McManus, Pascal Bernatchez, Leslie A Raffin, Heidi Paine, Cornelis van Breemen, George G S Sandor, Mitra Esfandiarei

Sildenafil Prevents Marfan-Associated Emphysema and Early Pulmonary Artery Dilation in Mice

西地那非可预防小鼠马凡氏综合征相关肺气肿和早期肺动脉扩张

Zoe White, Nadia Milad, Arash Y Tehrani, Jennifer Lamothe, James C Hogg, Mitra Esfandiarei, Michael Seidman, Steven Booth, Tillie-Louise Hackett, Mathieu C Morissette, Pascal Bernatchez