日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Allosteric Modulation of Pathological Ataxin-3 Aggregation: A Path to Spinocerebellar Ataxia Type-3 Therapies

病理性共济蛋白-3聚集的变构调节:脊髓小脑性共济失调3型治疗的途径

Silva, Alexandra; Duarte-Silva, Sara; Martins, Pedro M; Rodrigues, Beatriz; Serrenho, Débora; Vilasboas-Campos, Daniela; Teixeira-Castro, Andreia; Vieyto-Nuñez, Julio; Mieres-Perez, Joel; Figueiredo, Francisco; Podlasiak, Martyna; Van-der-Kellen, Tatiana; Fraga, Joana; Noble, James; Lantz, Carter; Sepanj, Niki; Monteiro-Fernandes, Daniela; Guerreiro, Sara; Neves-Carvalho, Andreia; Pereira-Sousa, Joana; Klärner, Frank-Gerrit; Schrader, Thomas; Loo, Joseph A; Pastore, Annalisa; Sanchez-Garcia, Elsa; Bitan, Gal; Carvalho, Ana Luísa; Maciel, Patrícia; Macedo-Ribeiro, Sandra

Learning the Biochemical Basis of Axonal Guidance: Using Caenorhabditis elegans as a Model.

了解轴突导向的生化基础:以秀丽隐杆线虫为模型

Teixeira-Castro Andreia, Sousa João Carlos, Vieira Cármen, Pereira-Sousa Joana, Vilasboas-Campos Daniela, Marques Fernanda, Pinto-do-Ó Perpétua, Maciel Patrícia

Profiling Microglia in a Mouse Model of Machado-Joseph Disease

对马查多-约瑟夫病小鼠模型中的小胶质细胞进行分析

Ana Bela Campos, Sara Duarte-Silva, Bruno Fernandes, Sofia Pereira das Neves, Fernanda Marques, Andreia Teixeira-Castro, Andreia Neves-Carvalho, Daniela Monteiro-Fernandes, Camila Cabral Portugal, Renato Socodato, Teresa Summavielle, António Francisco Ambrósio, João Bettencourt Relvas, Patrícia Maci

Data on the effects of Hyptis spp. and Lycium spp. plant extracts in C. elegans models of genetically determined neurodegenerative diseases

香薷属和枸杞属植物提取物对秀丽隐杆线虫遗传性神经退行性疾病模型的影响数据

Vilasboas-Campos, Daniela; Costa, Marta Daniela; Teixeira-Castro, Andreia; Rios, Rejaine; Silva, Fabiano Guimarães; Aierken, Aili; Zhang, Xiaoying; Bessa, Carlos; Dias, Alberto C P; Maciel, Patrícia

From Pathogenesis to Novel Therapeutics for Spinocerebellar Ataxia Type 3: Evading Potholes on the Way to Translation

从发病机制到脊髓小脑性共济失调3型的新型疗法:避开转化医学之路上的障碍

Da Silva, Jorge Diogo; Teixeira-Castro, Andreia; Maciel, Patrícia

Serotonergic signalling suppresses ataxin 3 aggregation and neurotoxicity in animal models of Machado-Joseph disease.

血清素能信号传导抑制 Machado-Joseph 病动物模型中的 ataxin 3 聚集和神经毒性

Teixeira-Castro Andreia, Jalles Ana, Esteves Sofia, Kang Soosung, da Silva Santos Liliana, Silva-Fernandes Anabela, Neto Mário F, Brielmann Renée M, Bessa Carlos, Duarte-Silva Sara, Miranda Adriana, Oliveira Stéphanie, Neves-Carvalho Andreia, Bessa João, Summavielle Teresa, Silverman Richard B, Oliveira Pedro, Morimoto Richard I, Maciel Patrícia

Neuron-specific proteotoxicity of mutant ataxin-3 in C. elegans: rescue by the DAF-16 and HSF-1 pathways

秀丽隐杆线虫中突变型共济蛋白-3的神经元特异性蛋白毒性:DAF-16和HSF-1通路可挽救其毒性

Teixeira-Castro, Andreia; Ailion, Michael; Jalles, Ana; Brignull, Heather R; Vilaça, João L; Dias, Nuno; Rodrigues, Pedro; Oliveira, João F; Neves-Carvalho, Andreia; Morimoto, Richard I; Maciel, Patrícia

Absence of ataxin-3 leads to enhanced stress response in C. elegans

缺乏共济蛋白-3会导致秀丽隐杆线虫的应激反应增强

Rodrigues, Ana João; Neves-Carvalho, Andreia; Teixeira-Castro, Andreia; Rokka, Anne; Corthals, Garry; Logarinho, Elsa; Maciel, Patrícia

Exclusion of mutations in the PRNP, JPH3, TBP, ATN1, CREBBP, POU3F2 and FTL genes as a cause of disease in Portuguese patients with a Huntington-like phenotype

排除PRNP、JPH3、TBP、ATN1、CREBBP、POU3F2和FTL基因突变作为葡萄牙亨廷顿样表型患者致病原因

Costa, Maria do Carmo; Teixeira-Castro, Andreia; Constante, Marco; Magalhães, Marina; Magalhães, Paula; Cerqueira, Joana; Vale, José; Passão, Vitorina; Barbosa, Célia; Robalo, Conceição; Coutinho, Paula; Barros, José; Santos, Manuela M; Sequeiros, Jorge; Maciel, Patrícia