日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Adult male patients with DKC1 mutations present early-onset pulmonary fibrosis and severe prognosis

携带 DKC1 基因突变的成年男性患者会出现早发性肺纤维化,预后不良。

Evrard, Ophélie; Philippot, Quentin; Kannengiesser, Caroline; Debray, Marie Pierre; Guyard, Alice; Fattori, Antonin; Schuller, Armelle; Nunes, Hilario; Montani, David; Bours, Vincent; Cottin, Vincent; Traclet, Julie; Benattia, Amira; Berthoux, Emilie; Daniel, Adrien; Yan-Min, Xu; Lainey, Elodie; Saussereau, Julien; Chelbi Viallon, Malika; Oudin, Claire; Morel, Héléne; Crestani, Bruno; Borie, Raphaël; Ba, Ibrahima

The phenotypic state of biallelic SERPINA1 Q0 variants in α(1)-antitrypsin deficiency

α(1)-抗胰蛋白酶缺乏症中双等位基因SERPINA1 Q0变异体的表型状态

Papiris, Spyros A; Veith, Martina; Ferrarotti, Ilaria; Balduyck, Malika-Leila; Filosa, Asia; Papaioannou, Andriana I; Lombard, Christine; Ottaviani, Stefania; Rovina, Nikoletta; Kolilekas, Lykourgos; Zerimech, Farid; Odou, Marie-Françoise; Dechomet, Magali; Prountzos, Spyridon; Kontopoulou, Christina; Kallieri, Maria; Cuvelier, Antoine; le Rouzic, Olivier; Apollonatou, Vasiliki; Antonogiannaki, Elvira-Markela; Osaba, Lourdes; Entrena, Edurne; Traclet, Julie; Weisenburger, Gaelle; Cottin, Vincent; Vogelmeier, Claus; Greulich, Timm; Monti, Maria Cristina; Mornex, Jean-François; Manali, Effrosyni D

Interstitial Lung Disease Associated with Anti-Ku Antibodies: A Case Series of 19 Patients

与抗Ku抗体相关的间质性肺病:19例患者病例系列研究

Petitgrand, Laure; Ahmad, Kaïs; Gamondès, Delphine; Diesler, Rémi; Fabien, Nicole; Gallay, Laure; Fort, Romain; Traclet, Julie; Lestelle, François; Chapurlat, Roland; Confavreux, Cyrille B; Durupt, Stéphane; Turquier, Ségolène; Si-Mohamed, Salim Aymeric; Coutant, Frédéric; Cottin, Vincent

Upfront triple therapy with parenteral prostanoid as a bridge to balloon pulmonary angioplasty in severe chronic thromboembolic pulmonary hypertension

对于重度慢性血栓栓塞性肺动脉高压患者,可采用肠外前列环素类药物进行一线三联疗法,作为球囊肺动脉成形术的过渡治疗。

Piliero, Nicolas; Salvat, Muriel; Finas, Mathieu; Curioz, Florence; Traclet, Julie; Ahmad, Kaïs; Bertoletti, Laurent; Vautrin, Estelle; Bouvaist, Hélène; Degano, Bruno

Pulmonary fibrosis in patients with autoimmune pulmonary alveolar proteinosis: a retrospective nationwide cohort study

自身免疫性肺泡蛋白沉积症患者的肺纤维化:一项回顾性全国队列研究

Guirriec, Yoann; Luque-Paz, David; Bernard, Gontran; Mabo, Axelle; Kerjouan, Mallorie; Ménard, Cédric; Monnier, Delphine; Nunes, Hilario; Uzunhan, Yurdagül; Reynaud-Gaubert, Martine; Bermudez, Julien; Borie, Raphaël; Crestani, Bruno; Traclet, Julie; Wémeau-Stervinou, Lidwine; Chenivesse, Cécile; Gomez, Emmanuel; Prévot, Grégoire; Bourdin, Arnaud; Bondue, Benjamin; Bergeron, Anne; Cottin, Vincent; Lederlin, Mathieu; Jouneau, Stéphane

Mepolizumab and benralizumab in patients with severe asthma and a history of eosinophilic granulomatosis with polyangiitis

美泊利单抗和贝那利珠单抗用于治疗重度哮喘且有嗜酸性肉芽肿性血管炎病史的患者

Desaintjean, Charlene; Ahmad, Kaïs; Traclet, Julie; Gerfaud-Valentin, Mathieu; Durel, Cecile-Audrey; Glerant, Jean-Charles; Hot, Arnaud; Lestelle, François; Mainbourg, Sabine; Nasser, Mouhamad; Seve, Pascal; Turquier, Ségolène; Devouassoux, Gilles; Cottin, Vincent

Bioreactance assessment of cardiac output lacks reliability for the follow-up of patients with pulmonary hypertension

生物阻抗法评估心输出量在肺动脉高压患者的随访中缺乏可靠性。

Turquier, Ségolène; Huot, Laure; Lamkhioued, Medhi; Subtil, Fabien; Traclet, Julie; Ahmad, Kais; Lestelle, François; Chauvelot, Louis; Cottin, Vincent; Mornex, Jean-François

Proteomic biomarkers for survival in systemic sclerosis-associated pulmonary hypertension

系统性硬化症相关肺动脉高压患者的生存蛋白质组学生物标志物

Mismetti, Valentine; Delavenne, Xavier; Montani, David; Bezzeghoud, Souad; Delezay, Olivier; Hodin, Sophie; Launay, David; Marchand-Adam, Sylvain; Nunes, Hilario; Ollier, Edouard; Reynaud-Gaubert, Martine; Pastre, Jean; Traclet, Julie; Quetant, Sébastien; Zeghmar, Sabrina; Bertoletti, Laurent; Cottin, Vincent

An emerging phenotype of pulmonary arterial hypertension patients carrying SOX17 variants

携带SOX17变异的肺动脉高压患者的一种新表型

Montani, David; Lechartier, Benoit; Girerd, Barbara; Eyries, Mélanie; Ghigna, Maria-Rosa; Savale, Laurent; Jaïs, Xavier; Seferian, Andrei; Jevnikar, Mitja; Boucly, Athénais; Riou, Marianne; Traclet, Julie; Chaouat, Ari; Levy, Maryline; Le Pavec, Jerome; Fadel, Elie; Perros, Frédéric; Soubrier, Florent; Remy-Jardin, Martine; Sitbon, Olivier; Bonnet, Damien; Humbert, Marc

COVID-19 in Patients with Pulmonary Hypertension: A National Prospective Cohort Study

COVID-19 与肺动脉高压患者:一项全国前瞻性队列研究

Montani, David; Certain, Marie-Caroline; Weatherald, Jason; Jaïs, Xavier; Bulifon, Sophie; Noel-Savina, Elise; Nieves, Ana; Renard, Sébastien; Traclet, Julie; Bouvaist, Hélène; Riou, Marianne; de Groote, Pascal; Moceri, Pamela; Bertoletti, Laurent; Favrolt, Nicolas; Guillaumot, Anne; Jutant, Etienne-Marie; Beurnier, Antoine; Boucly, Athénaïs; Ebstein, Nathan; Jevnikar, Mitja; Pichon, Jérémie; Keddache, Sophia; Preda, Mariana; Roche, Anne; Solinas, Sabina; Seferian, Andrei; Reynaud-Gaubert, Martine; Cottin, Vincent; Savale, Laurent; Humbert, Marc; Sitbon, Olivier