日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Assessing bleeding risk by thromboelastography when automated platelet count fails due to giant platelets

当由于巨型血小板导致自动血小板计数失败时,可通过血栓弹力图评估出血风险。

Ye, Zhan; Sami, Farhan; Hinojosa, Oscar; Zheng, Liang; Gu, Hongyan; Zhao, Xinyang; Dasgupta, Amitava; Zheng, X Long

Restoring VWF multimerization via endothelial gene therapy: A minimalist yet mechanistically precise approach

通过内皮细胞基因疗法恢复VWF多聚化:一种简约而机制精准的方法

Zheng, X Long

Caplacizumab use in immune-mediated thrombotic thrombocytopenic purpura: an international multicentre retrospective Cohort study (The Capla 1000+ project)

Caplacizumab 在免疫介导的血栓性血小板减少性紫癜中的应用:一项国际多中心回顾性队列研究(Capla 1000+ 项目)

Coppo, Paul; Bubenheim, Michael; Benhamou, Ygal; Völker, Linus; Brinkkötter, Paul; Kühne, Lucas; Knöbl, Paul; Mingot-Castellano, Maria Eva; Pascual-Izquierdo, Cristina; de la Rubia, Javier; Del Rio Garma, Julio; Chaturvedi, Shruti; Masias, Camila; Mazepa, Marshall; Zheng, X Long; Sinkovits, György; Réti, Marienn; Patriquin, Christopher J; Pavenski, Katerina; Boechat, Tiago; Farias, João; Oliveira Ribeiro, Eduardo Flavio; Lobo de Andrade, Michaela Larissa; Veyradier, Agnès; Joly, Bérangère; Bouzid, Raïda; Sakai, Kazuya; Matsumoto, Masanori; Agosti, Pasquale; Mancini, Ilaria; Peyvandi, Flora; Gavriilaki, Eleni; Stubbs, Matthew; Hmaid, Amjad; Cataland, Spero; Lämmle, Bernhard; Scully, Marie

Arginine Methylation by PRMT1 Affects ADAMTS13 Secretion and Enzymatic Activity

PRMT1介导的精氨酸甲基化影响ADAMTS13的分泌和酶活性

Liu, Szumam; Ma, Min; Qu, Jun; Muia, Joshua; Wu, Zhijian; Bonnez, Quintijn; Vanhoorelbeke, Karen; Zheng, Liang; Zhao, Xinyang; Zheng, X Long

Relapse-free survival is progressively shortened in a subset of Black patients with immune-mediated TTP treated in the rituximab era

在利妥昔单抗时代接受治疗的部分黑人免疫介导性血栓性血小板减少性紫癜(TTP)患者的无复发生存期逐渐缩短。

Fatola, Ayotola; Evans, Michael D; Brown, Jenna; Davis, Elizabeth; Johnson, Andrew; Antun, Ana G; Farland, Andrew M; Woods, Ryan; Metjian, Ara; Park, Yara A; de Ridder, Gustaaf; Gibson, Briana; Kasthuri, Raj S; Liles, Darla K; Eubanks, Susan; Akwaa, Frank; Clover, Todd; Kreuziger, Lisa Baumann; Sadler, J Evan; Sridharan, Meera; Go, Ronald S; McCrae, Keith R; Upreti, Harsh Vardhan; Lim, Ming Y; Kocher, Nicole K; Gangaraju, Radhika; Zheng, X Long; Raval, Jay S; Masias, Camila; Cataland, Spero R; Mazepa, Marshall; Chaturvedi, Shruti

A mutant complement factor H (W1183R) enhances proteolytic cleavage of von Willebrand factor by ADAMTS-13 under shear

突变型补体因子H (W1183R) 在剪切力作用下增强ADAMTS-13对血管性血友病因子的蛋白水解切割。

Cao, Wenjing; Liu, Yi; Zhang, X Frank; Zheng, X Long

SARS-CoV-2 ORF7a activates the endothelium to release von Willebrand factor that promotes thrombosis.

SARS-CoV-2 ORF7a 激活内皮细胞释放血管性血友病因子,从而促进血栓形成

Zhang Quan, Huang Xiaohu, Lee Hangnoh, Lee Jin-Gu, Liu Szumam, Limbu Shiwani, Basu Malay K, van de Leemput Joyce, D'Agnillo Felice, Han Zhe, Zheng X Long

Modeling ANKRD26 5'-UTR mutation-related thrombocytopenia

ANKRD26 5'-UTR 突变相关血小板减少症建模

Zheng, Liang; Wu, Zhijian; Yada, Noritaka; Liu, Szumam; Lin, Cindy; Bignotti, Antonia; Zhao, Xinyang; Zheng, X Long

Genetic mutations in lymphocytic variant of hypereosinophilic syndrome: study of five siblings

高嗜酸性粒细胞综合征淋巴细胞变异型的基因突变:对五名兄弟姐妹的研究

Walkenhorst, Molly; Basu, Malay K; Cui, Wei; Kumar, Manish; Vallurupalli, Anusha; Sitek, Andrea; Zhao, Xinyang; Zheng, X Long; Zhang, Da

Targeting neutrophil extracellular trap accumulation under flow in patients with immune-mediated thrombotic thrombocytopenic purpura

针对免疫介导的血栓性血小板减少性紫癜患者流动条件下中性粒细胞胞外陷阱的积累进行治疗

Yada, Noritaka; Zhang, Quan; Bignotti, Antonia; Gralnek, Sarah H; Sosnovske, Dennis; Hogan, Keenan; Ye, Zhan; Zheng, Liang; Zheng, X Long